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Image of a neural disease that would cause high-frequency hearing loss.

How often do you contemplate your nervous system? Most likely not all that regularly. Generally, you wouldn’t have to worry about how your neurons are communicating signals to the nerves of your body. But when those nerves begin to misfire – that is when something fails – you begin to pay a lot more attention to your nervous system.

One particular disease known as Charot-Marie-Tooth Disease which typically affects the extremities can also have a pretty wide-scale impact on the whole nervous system. And there’s some evidence to suggest that CMT can also lead to high-frequency loss of hearing.

What Is Charcot-Marie-Tooth Disease?

Charcot-Marie-Tooth disease is a set of inherited disorders. The protective sheathing surrounding the nerves malfunction due to a genetic disorder.

As a result, the impulses sent from your brain to those nerves (and from those nerves back to your brain) don’t work all that well. A loss in motor function and sensation can be the outcome.

A blend of genetic elements typically leads to the expression of symptoms, so CMT can be present in a number of varieties. For most people who have CMT, symptoms begin in the feet and can work their way up into their arms. And, high-frequency hearing loss, strangely, has a high rate of occurrence in those with CMT.

The Cochlear Nerve: A Connection Between CMT and Loss of Hearing

The link between CMT and hearing loss has always been colloquially established (that is, everybody knows somebody who has a story about it – at least within the CMT culture). And it was hard to recognize the connection between loss of sensation in the legs and problems with the ears.

The connection was firmly established by a scientific study just recently when a group of researchers examined 79 people with CMT at the University of Iowa Hospitals and Clinics.

The results were quite conclusive. Almost everyone who has CMT passed their low and moderate frequency hearing exams with flying colors. But high-frequency sounds (in the moderate region particularly) were effortlessly heard by all of the participants. high-frequency hearing loss, according to this study, is likely to be connected to CMT.

What is The Cause of Hearing Loss And How Can it be Addressed?

The connection between high-frequency loss of hearing and CMT could, at first, seem puzzling. Like all other parts of your body rely on properly functioning nerves. Your ears are the same.

The theory is, CMT affects the cochlear nerve so noises in the high-frequency range aren’t able to be interpreted. Anyone with this type of hearing loss will have a hard time hearing some sounds, and that includes voices. Particularly, understand voices in crowded or noisy rooms can be a real obstacle.

This form of hearing loss is commonly treated with hearing aids. CMT has no renowned cure. Modern hearing aids can offer significant assistance in terms of fighting the effects of high-frequency hearing loss, isolating only those ranges of sounds to boost. The majority of modern hearing aids can also work well in noisy environments.

Multiple Reasons For Hearing Loss

Experts still aren’t completely certain why CMT and loss of hearing seem to co-exist quite so often (above and beyond their untested theory). But this type of hearing loss can be effectively managed with hearing aids. That’s why countless individuals who have CMT will make time to get a consultation with a hearing care professional and get fitted for a custom hearing aid.

Hearing loss symptoms can occur for numerous reasons. In many instances, hearing loss is caused by excess exposure to damaging sounds. In other circumstances, loss of hearing may be the result of a blockage. It also appears that CMT is another possible cause.

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